ICD-10 code for pulmonic congenital stenosis

The ICD-10-CM code for pulmonic congenital stenosis is Q22.1 (Congenital pulmonary valve stenosis). The official index lists 2 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q22.1.

Within Q22 (congenital malformations of pulmonary and tricuspid valves), Q22.1 is specifically for congenital pulmonary valve stenosis. Related codes cover pulmonary valve atresia (Q22.0), congenital pulmonary valve insufficiency (Q22.2), other congenital malformations of pulmonary valve (Q22.3), congenital tricuspid stenosis (Q22.4), Ebstein's anomaly (Q22.5), Hypoplastic right heart syndrome (Q22.6), other congenital malformations of tricuspid valve (Q22.8) and congenital malformation of tricuspid valve, unspecified (Q22.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.