ICD-10-CM 2027
ICD-10 code for Rhizomelic chondrodysplasia punctata
From the official ICD-10-CM alphabetic index entry “Rhizomelic chondrodysplasia punctata”. Page updated September 29, 2026.
About coding Rhizomelic chondrodysplasia punctata
The ICD-10-CM code for Rhizomelic chondrodysplasia punctata is E71.540 (Rhizomelic chondrodysplasia punctata).
Within E71.54 (other peroxisomal disorders), E71.540 is specifically for Rhizomelic chondrodysplasia punctata. Related codes cover Zellweger-like syndrome (E71.541), other group 3 peroxisomal disorders (E71.542) and other peroxisomal disorders (E71.548).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Rhizomelic chondrodysplasia punctata ICD-10 codes
What is the ICD-10 code for Rhizomelic chondrodysplasia punctata?
- E71.540 — Rhizomelic chondrodysplasia punctata.
Is E71.540 billable?
- Yes. E71.540 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E71.540 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E71.540 as a principal diagnosis.
Is E71.540 a CC or MCC?
- E71.540 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.