ICD-10-CM 2027
ICD-10 code for Rieger anomaly or syndrome
From the official ICD-10-CM alphabetic index entry “Rieger anomaly or syndrome”. Page updated September 29, 2026.
About coding Rieger anomaly or syndrome
The ICD-10-CM code for Rieger anomaly or syndrome is Q13.81 (Rieger anomaly).
Within Q13.8 (other congenital malformations of anterior segment of eye), Q13.81 is specifically for Rieger anomaly. Related codes cover other congenital malformations of anterior segment of eye (Q13.89).
Use an additional code for associated glaucoma (H42).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
Common questions about Rieger anomaly or syndrome ICD-10 codes
What is the ICD-10 code for Rieger anomaly or syndrome?
- Q13.81 — Rieger anomaly.
Is Q13.81 billable?
- Yes. Q13.81 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q13.81 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q13.81 as a principal diagnosis.
Is Q13.81 a CC or MCC?
- No. Q13.81 is neither a CC nor an MCC under MS-DRG v44.0.