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ICD-10-CM 2027 diagnosis code

Q13.81Rieger anomaly

✓ Billable / specificPOA exempt

Q13.81 is a valid, billable ICD-10-CM code for rieger anomaly. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.

Looking up by condition? See ICD-10 code for Rieger anomaly or syndrome.

Code last changed in FY2025 (effective October 1, 2024). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About Q13.81

Q13.81 is the ICD-10-CM diagnosis code for Rieger anomaly. It belongs to category Q13 (congenital malformations of anterior segment of eye), block Q10-Q18 (congenital malformations of eye, ear, face and neck) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q13.8 (other congenital malformations of anterior segment of eye), Q13.81 is specifically for Rieger anomaly. Related codes cover other congenital malformations of anterior segment of eye (Q13.89).

Use an additional code for associated glaucoma (H42).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 124 (Other Disorders of the Eye with MCC or Thrombolytic Agent, relative weight 1.2471) and DRG 125 (Other Disorders of the Eye without MCC, relative weight 0.7702), in MDC 02 (Diseases and Disorders of the Eye), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015, and changed in FY2025 (title revised).

Before ICD-10, this condition was coded in ICD-9-CM as 743.44 (specified congenital anomalies of anterior chamber, chamber angle, and related structures).

Coding notes

Applicable toConditions and synonyms classified to this code
  • Axenfeld-Rieger syndrome
Use additional codeAdd a secondary code to fully describe the condition
  • code for associated glaucoma (H42)
Code alsoTwo codes may be needed; sequencing depends on circumstances
  • any other associated congenital malformations such as cardiac defects

Notes that apply from higher levels

Instructions written at a parent level also apply to Q13.81.

Broader instructions also apply from Q10-Q18 Congenital malformations of eye, ear, face and neck and Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.

Alphabetic index entries

4 entries

Terms in the official ICD-10-CM index that lead to Q13.81.

Codes whose notes reference Q13.81

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

ICD-9-CM equivalent

Converter →
  • 743.44Specified congenital anomalies of anterior chamber, chamber angle, and related structuresapproximate

From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
  • FY2025 (effective 10/1/2024): Title revised — was “Rieger's anomaly”

Common questions about Q13.81

Is Q13.81 billable?

Yes. Q13.81 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can Q13.81 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict Q13.81 as a principal diagnosis.

Is Q13.81 a CC or MCC?

No. Q13.81 is neither a CC nor an MCC under MS-DRG v44.0.

What DRG does Q13.81 group to?

Q13.81 is used in the MS-DRG v44.0 logic for MS-DRG 124 (Other Disorders of the Eye with MCC or Thrombolytic Agent) and MS-DRG 125 (Other Disorders of the Eye without MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.

What is the ICD-9 code for Q13.81?

The CMS General Equivalence Mappings map Q13.81 to ICD-9-CM 743.44.