ICD-10-CM 2027
ICD-10 code for sideroblastic anemia
From the official ICD-10-CM alphabetic index entry “Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › sideroblastic”. Page updated September 29, 2026.
About coding sideroblastic anemia
The ICD-10-CM code for sideroblastic anemia is D64.3 (Other sideroblastic anemias). The official index lists 7 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on D64.3.
Within D64, choose D64.3 (Other sideroblastic anemias) only when documentation doesn't support a more specific option: hereditary sideroblastic anemia (D64.0), secondary sideroblastic anemia due to disease (D64.1), secondary sideroblastic anemia due to drugs and toxins (D64.2), congenital dyserythropoietic anemia (D64.4), other specified anemias (D64.8) and anemia, unspecified (D64.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 811 (Red Blood Cell Disorders with MCC, relative weight 1.3988) and DRG 812 (Red Blood Cell Disorders without MCC, relative weight 0.9234), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific sideroblastic anemia codes (official index)
- hereditary D64.0 — Hereditary sideroblastic anemia
- hypochromic, sex-linked D64.0 — Hereditary sideroblastic anemia
- pyridoxine-responsive NEC D64.3 — Other sideroblastic anemias
- refractory D46.1 — Refractory anemia with ring sideroblasts
- secondary (due to)
- disease D64.1 — Secondary sideroblastic anemia due to disease
- drugs and toxins D64.2 — Secondary sideroblastic anemia due to drugs and toxins
- specified type NEC D64.3 — Other sideroblastic anemias
Common questions about sideroblastic anemia ICD-10 codes
What is the ICD-10 code for sideroblastic anemia?
- D64.3 — Other sideroblastic anemias. More specific codes apply when the documentation supports them: D64.0, D64.0, D64.3, D46.1 and others below.
What is the ICD-10 code for hereditary sideroblastic anemia?
- D64.0 — Hereditary sideroblastic anemia.
What is the ICD-10 code for pyridoxine-responsive nec sideroblastic anemia?
- D64.3 — Other sideroblastic anemias.
What is the ICD-10 code for refractory sideroblastic anemia?
- D46.1 — Refractory anemia with ring sideroblasts.
Is D64.3 billable?
- Yes. D64.3 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D64.3 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D64.3 as a principal diagnosis.
Is D64.3 a CC or MCC?
- No. D64.3 is neither a CC nor an MCC under MS-DRG v44.0.