D64.4Congenital dyserythropoietic anemia

D64.4 is the ICD-10-CM diagnosis code for congenital dyserythropoietic anemia. It belongs to category D64 (other anemias), block D60-D64 (aplastic and other anemias and other bone marrow failure syndromes) and chapter 3 (diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within D64 (other anemias), D64.4 is specifically for congenital dyserythropoietic anemia. Related codes cover hereditary sideroblastic anemia (D64.0), secondary sideroblastic anemia due to disease (D64.1), secondary sideroblastic anemia due to drugs and toxins (D64.2), other sideroblastic anemias (D64.3), other specified anemias (D64.8) and anemia, unspecified (D64.9).

Don't report D64.4 together with the conditions in its Excludes1 note: Blackfan-Diamond syndrome (D61.01) and Di Guglielmo's disease (C94.0).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 811 (Red Blood Cell Disorders with MCC, relative weight 1.3988) and DRG 812 (Red Blood Cell Disorders without MCC, relative weight 0.9234), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 285.8 (other specified anemias).