ICD-10-CM 2027
ICD-10 code for Simons' disease
From the official ICD-10-CM alphabetic index entry “Disease, diseased › Simons' (progressive lipodystrophy)”. Page updated September 29, 2026.
About coding Simons' disease
The ICD-10-CM code for Simons' disease is E88.11 (Partial lipodystrophy).
Within E88.1 (lipodystrophy, not elsewhere classified), E88.11 is specifically for partial lipodystrophy. Related codes cover lipodystrophy, unspecified (E88.10), generalized lipodystrophy (E88.12), localized lipodystrophy (E88.13), HIV-associated lipodystrophy (E88.14) and other lipodystrophy, not elsewhere classified (E88.19).
Use an additional code for: codes for associated conditions.
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
Common questions about Simons' disease ICD-10 codes
What is the ICD-10 code for Simons' disease?
- E88.11 — Partial lipodystrophy.
Is E88.11 billable?
- Yes. E88.11 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E88.11 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E88.11 as a principal diagnosis.
Is E88.11 a CC or MCC?
- No. E88.11 is neither a CC nor an MCC under MS-DRG v44.0.