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ICD-10-CM 2027

ICD-10 code for SMEI

G40.83

Dravet syndrome

Header — needs a more specific code

From the official ICD-10-CM alphabetic index entry “SMEI (severe myoclonic epilepsy in infancy)”. Page updated September 29, 2026.

About coding SMEI

The ICD-10-CM code for SMEI is G40.83 (Dravet syndrome).

Within G40.8 (other epilepsy and recurrent seizures), G40.83 is specifically for Dravet syndrome. Related codes cover other epilepsy (G40.80), Lennox-Gastaut syndrome (G40.81), epileptic spasms (G40.82), KCNQ2-related epilepsy (G40.84) and other seizures (G40.89).

To report this condition, pick the subcode that matches the documentation: G40.833 (intractable, with status epilepticus) and G40.834 (intractable, without status epilepticus).

It was added in FY2021, effective October 1, 2020.

Common questions about SMEI ICD-10 codes

What is the ICD-10 code for SMEI?

G40.83 — Dravet syndrome (a header code; report a more specific subcode).

Is G40.83 billable?

No. G40.83 is a header code. Report one of its more specific subcodes instead.