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ICD-10-CM 2027 diagnosis code

G40.83Dravet syndrome

Not billable — use a more specific code

G40.83 is a header code, so it can't be reported by itself. Choose one of the 2 more specific codes beneath it.

Looking up by condition? See ICD-10 code for PMEI, ICD-10 code for SMEI.

Code last changed in FY2021 (effective October 1, 2020). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About G40.83

G40.83 is the ICD-10-CM diagnosis code for Dravet syndrome. It belongs to category G40 (epilepsy and recurrent seizures), block G40-G47 (episodic and paroxysmal disorders) and chapter 6 (diseases of the nervous system). It is a header code, so it can't be reported by itself; one of its 2 subcodes must be used instead.

Within G40.8 (other epilepsy and recurrent seizures), G40.83 is specifically for Dravet syndrome. Related codes cover other epilepsy (G40.80), Lennox-Gastaut syndrome (G40.81), epileptic spasms (G40.82), KCNQ2-related epilepsy (G40.84) and other seizures (G40.89).

To report this condition, pick the subcode that matches the documentation: G40.833 (intractable, with status epilepticus) and G40.834 (intractable, without status epilepticus).

It was added in FY2021, effective October 1, 2020.

Specific codes under G40.83

Coding notes

Applicable toConditions and synonyms classified to this code
  • Polymorphic epilepsy in infancy (PMEI)
  • Severe myoclonic epilepsy in infancy (SMEI)

Notes that apply from higher levels

Instructions written at a parent level also apply to G40.83.

› From G40 Epilepsy and recurrent seizures
Note
  • the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled
Excludes1
  • conversion disorder with seizures (F44.5)
  • convulsions NOS (R56.9)
  • post traumatic seizures (R56.1)
  • seizure (convulsive) NOS (R56.9)
  • seizure of newborn (P90)
Excludes2

Broader instructions also apply from Chapter 6: Diseases of the nervous system.

Alphabetic index entries

4 entries

Terms in the official ICD-10-CM index that lead to G40.83.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2021 (effective 10/1/2020): Added
  • No changes since FY2021.

Common questions about G40.83

Is G40.83 billable?

No. G40.83 is a header code. Report one of its more specific subcodes instead.