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ICD-10-CM 2027 diagnosis code

D68.01Von Willebrand disease, type 1

✓ Billable / specificCC — complication/comorbidity

D68.01 is a valid, billable ICD-10-CM code for von willebrand disease, type 1. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.

Code last changed in FY2023 (effective October 1, 2022). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About D68.01

D68.01 is the ICD-10-CM diagnosis code for von Willebrand disease, type 1. It belongs to category D68 (other coagulation defects), block D65-D69 (coagulation defects, purpura and other hemorrhagic conditions) and chapter 3 (diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within D68.0 (von Willebrand disease), D68.01 is specifically for von Willebrand disease, type 1. Related codes cover unspecified (D68.00), type 2 (D68.02), type 3 (D68.03), acquired von Willebrand disease (D68.04) and other von Willebrand disease (D68.09).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 813 (Coagulation Disorders, relative weight 1.5257), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It was added in FY2023, effective October 1, 2022.

Coding notes

Applicable toConditions and synonyms classified to this code
  • Partial quantitative deficiency of von Willebrand factor
  • Type 1C von Willebrand disease

Notes that apply from higher levels

Instructions written at a parent level also apply to D68.01.

› From D68.0 Von Willebrand disease
Excludes1
  • capillary fragility (hereditary) (D69.8)
  • factor VIII deficiency NOS (D66)
  • factor VIII deficiency with functional defect (D66)
› From D68 Other coagulation defects
Excludes1
  • abnormal coagulation profile NOS (R79.1)
Excludes2
  • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
  • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

Broader instructions also apply from Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism.

Alphabetic index entries

3 entries

Terms in the official ICD-10-CM index that lead to D68.01.

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

MDC 16 · Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2023 (effective 10/1/2022): Added
  • No changes since FY2023.

Common questions about D68.01

Is D68.01 billable?

Yes. D68.01 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can D68.01 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict D68.01 as a principal diagnosis.

Is D68.01 a CC or MCC?

D68.01 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.

What DRG does D68.01 group to?

D68.01 is used in the MS-DRG v44.0 logic for MS-DRG 813 (Coagulation Disorders). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.