G04.3Acute necrotizing hemorrhagic encephalopathy

G04.3 is the ICD-10-CM diagnosis code for acute necrotizing hemorrhagic encephalopathy. It belongs to category G04 (encephalitis, myelitis and encephalomyelitis), block G00-G09 (inflammatory diseases of the central nervous system) and chapter 6 (diseases of the nervous system). It is a header code, so it can't be reported by itself; one of its 4 subcodes must be used instead.

Within G04 (encephalitis, myelitis and encephalomyelitis), G04.3 is specifically for acute necrotizing hemorrhagic encephalopathy. Related codes cover acute disseminated encephalitis and encephalomyelitis (ADEM) (G04.0), tropical spastic paraplegia (G04.1), bacterial meningoencephalitis and meningomyelitis, not elsewhere classified (G04.2), other encephalitis, myelitis and encephalomyelitis (G04.8) and unspecified (G04.9).

To report this condition, pick the subcode that matches the documentation: G04.30 (unspecified), G04.31 (encephalopathy), G04.32 (encephalopathy) and G04.39 (encephalopathy).

Don't report G04.3 together with the conditions in its Excludes1 note: acute disseminated encephalitis and encephalomyelitis (G04.0-).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.