G99.0Autonomic neuropathy in diseases classified elsewhere

G99.0 is the ICD-10-CM diagnosis code for autonomic neuropathy in diseases classified elsewhere. It belongs to category G99 (other disorders of nervous system in diseases classified elsewhere), block G89-G99 (other disorders of the nervous system) and chapter 6 (diseases of the nervous system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within G99 (other disorders of nervous system in diseases classified elsewhere), G99.0 is specifically for autonomic neuropathy in diseases classified elsewhere. Related codes cover myelopathy in diseases classified elsewhere (G99.2) and other specified disorders of nervous system in diseases classified elsewhere (G99.8).

Don't report G99.0 together with the conditions in its Excludes1 note: diabetic autonomic neuropathy (E08-E13 with .43).

Code first underlying disease, such as: amyloidosis (E85.-), gout (M1A.-, M10.-) and hyperthyroidism (E05.-).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 073 (Cranial and Peripheral Nerve Disorders with MCC, relative weight 1.5779) and DRG 074 (Cranial and Peripheral Nerve Disorders without MCC, relative weight 1.0173), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is a manifestation code, so it describes the effect of an underlying disease and can't be the principal diagnosis. Code the underlying condition first.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 337.1 (peripheral autonomic neuropathy in disorders classified elsewhere).