ICD-10-CM 2027 diagnosis code

I01Rheumatic fever with heart involvement

Not billable — use a more specific code

I01 is a header code, so it can't be reported by itself. Choose one of the 5 more specific codes beneath it.

Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About I01

I01 is the ICD-10-CM diagnosis code for rheumatic fever with heart involvement. It belongs to block I00-I02 (acute rheumatic fever) and chapter 9 (diseases of the circulatory system). It is a header code, so it can't be reported by itself; one of its 5 subcodes must be used instead.

To report this condition, pick the subcode that matches the documentation: I01.0 (pericarditis), I01.1 (endocarditis), I01.2 (myocarditis), I01.8 (disease) and I01.9 (unspecified).

Don't report I01 together with the conditions in its Excludes1 note: chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process..

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Specific codes under I01

Coding notes

Excludes1Not coded here — never report together with this code

chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.

Notes that apply from higher levels

Instructions written at a parent level also apply to I01.

Broader instructions also apply from Chapter 9: Diseases of the circulatory system.

Alphabetic index entries

1 entries

Terms in the official ICD-10-CM index that lead to I01.

Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor) › rheumatic (active) (acute) (chronic) (subacute) › active with heart involvement

Code history

2016
2017
2018
2019
2020
2021
2022
2023
2024
2025
2026
2027

FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
No changes since FY2016.

Common questions about I01

Is I01 billable?: No. I01 is a header code. Report one of its more specific subcodes instead.