I01.8Other acute rheumatic heart disease

I01.8 is the ICD-10-CM diagnosis code for other acute rheumatic heart disease. It belongs to category I01 (rheumatic fever with heart involvement), block I00-I02 (acute rheumatic fever) and chapter 9 (diseases of the circulatory system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within I01, choose I01.8 (Other acute rheumatic heart disease) only when documentation doesn't support a more specific option: acute rheumatic pericarditis (I01.0), acute rheumatic endocarditis (I01.1), acute rheumatic myocarditis (I01.2) and acute rheumatic heart disease, unspecified (I01.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 314 (Other Circulatory System Diagnoses with MCC, relative weight 2.0873), DRG 315 (Other Circulatory System Diagnoses with CC, relative weight 0.9508) and DRG 316 (Other Circulatory System Diagnoses without CC/MCC, relative weight 0.6677), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 391.8 (other acute rheumatic heart disease).