J84.178Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

J84.178 is the ICD-10-CM diagnosis code for other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere. It belongs to category J84 (other interstitial pulmonary diseases), block J80-J84 (other respiratory diseases principally affecting the interstitium) and chapter 10 (diseases of the respiratory system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within J84.17, choose J84.178 (Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere) only when documentation doesn't support a more specific option: interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere (J84.170).

Code first underlying disease, such as: progressive systemic sclerosis (M34.0), rheumatoid arthritis (M05.00-M06.9) and systemic lupus erythematosis (M32.0-M32.9).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 196 (Interstitial Lung Disease with MCC, relative weight 1.8336), DRG 197 (Interstitial Lung Disease with CC, relative weight 0.9492) and DRG 198 (Interstitial Lung Disease without CC/MCC, relative weight 0.7259), in MDC 04 (Diseases and Disorders of the Respiratory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is a manifestation code, so it describes the effect of an underlying disease and can't be the principal diagnosis. Code the underlying condition first.

It was added in FY2021, effective October 1, 2020.