N01Rapidly progressive nephritic syndrome

N01 is the ICD-10-CM diagnosis code for rapidly progressive nephritic syndrome. It belongs to block N00-N08 (glomerular diseases) and chapter 14 (diseases of the genitourinary system). It is a header code, so it can't be reported by itself; one of its 11 subcodes must be used instead.

To report this condition, pick the subcode that matches the documentation: N01.0 (with minor glomerular abnormality), N01.1 (with focal and segmental glomerular lesions), N01.2 (with diffuse membranous glomerulonephritis), N01.3 (with diffuse mesangial proliferative glomerulonephritis), N01.4 (with diffuse endocapillary proliferative glomerulonephritis), N01.5 (with diffuse mesangiocapillary glomerulonephritis), N01.6 (with dense deposit disease), N01.7 (with diffuse crescentic glomerulonephritis) and 3 more.

Don't report N01 together with the conditions in its Excludes1 note: nephritic syndrome NOS (N05.-).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.