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ICD-10-CM 2027 diagnosis code

N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormality

✓ Billable / specificMCC — major complication/comorbidity

N01.0 is a valid, billable ICD-10-CM code for rapidly progressive nephritic syndrome with minor glomerular abnormality. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.Short description: Rapidly progr nephritic syndrome w minor glomerular abnlt

Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About N01.0

N01.0 is the ICD-10-CM diagnosis code for rapidly progressive nephritic syndrome with minor glomerular abnormality. It belongs to category N01 (rapidly progressive nephritic syndrome), block N00-N08 (glomerular diseases) and chapter 14 (diseases of the genitourinary system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within N01 (rapidly progressive nephritic syndrome), N01.0 is specifically for rapidly progressive nephritic syndrome with minor glomerular abnormality. Related codes cover with focal and segmental glomerular lesions (N01.1), with diffuse membranous glomerulonephritis (N01.2), with diffuse mesangial proliferative glomerulonephritis (N01.3), with diffuse endocapillary proliferative glomerulonephritis (N01.4), with diffuse mesangiocapillary glomerulonephritis (N01.5), with dense deposit disease (N01.6), with diffuse crescentic glomerulonephritis (N01.7), with other morphologic changes (N01.8) and 2 more.

As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 698 (Other Kidney and Urinary Tract Diagnoses with MCC, relative weight 1.6398), DRG 699 (Other Kidney and Urinary Tract Diagnoses with CC, relative weight 1.0003), DRG 700 (Other Kidney and Urinary Tract Diagnoses without CC/MCC, relative weight 0.6741), DRG 791 (Prematurity with Major Problems, relative weight 4.1075) and DRG 793 (Full Term Neonate with Major Problems, relative weight 4.2195), in MDC 11 (Diseases and Disorders of the Kidney and Urinary Tract) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 580.4 (acute glomerulonephritis with lesion of rapidly progressive glomerulonephritis).

Coding notes

Applicable toConditions and synonyms classified to this code
  • Rapidly progressive nephritic syndrome with minimal change lesion

Notes that apply from higher levels

Instructions written at a parent level also apply to N01.0.

› From N01 Rapidly progressive nephritic syndrome
Includes
  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis
Excludes1
  • nephritic syndrome NOS (N05.-)

Broader instructions also apply from N00-N08 Glomerular diseases and Chapter 14: Diseases of the genitourinary system.

Alphabetic index entries

1 entries

Terms in the official ICD-10-CM index that lead to N01.0.

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

MDC 15 · Newborns and Other Neonates with Conditions Originating in the Perinatal Period

MDC 15 · Newborns and Other Neonates with Conditions Originating in the Perinatal Period

ICD-9-CM equivalent

Converter →
  • 580.4Acute glomerulonephritis with lesion of rapidly progressive glomerulonephritisapproximate

From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
  • No changes since FY2016.

Common questions about N01.0

Is N01.0 billable?

Yes. N01.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can N01.0 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict N01.0 as a principal diagnosis.

Is N01.0 a CC or MCC?

N01.0 is an MCC (major complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.

What DRG does N01.0 group to?

N01.0 is used in the MS-DRG v44.0 logic for MS-DRG 698 (Other Kidney and Urinary Tract Diagnoses with MCC), MS-DRG 699 (Other Kidney and Urinary Tract Diagnoses with CC), MS-DRG 700 (Other Kidney and Urinary Tract Diagnoses without CC/MCC), MS-DRG 791 (Prematurity with Major Problems) and MS-DRG 793 (Full Term Neonate with Major Problems). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.

What is the ICD-9 code for N01.0?

The CMS General Equivalence Mappings map N01.0 to ICD-9-CM 580.4.