ICD-10-CM 2027 diagnosis code
N04Nephrotic syndrome
N04 is a header code, so it can't be reported by itself. Choose one of the 12 more specific codes beneath it.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About N04
N04 is the ICD-10-CM diagnosis code for nephrotic syndrome. It belongs to block N00-N08 (glomerular diseases) and chapter 14 (diseases of the genitourinary system). It is a header code, so it can't be reported by itself; one of its 12 subcodes must be used instead.
To report this condition, pick the subcode that matches the documentation: N04.0 (with minor glomerular abnormality), N04.1 (with focal and segmental glomerular lesions), N04.2 (with diffuse membranous glomerulonephritis), N04.3 (with diffuse mesangial proliferative glomerulonephritis), N04.4 (with diffuse endocapillary proliferative glomerulonephritis), N04.5 (with diffuse mesangiocapillary glomerulonephritis), N04.6 (with dense deposit disease), N04.7 (with diffuse crescentic glomerulonephritis) and 4 more.
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Specific codes under N04
- N04.0Nephrotic syndrome with minor glomerular abnormalityBillable
- N04.1Nephrotic syndrome with focal and segmental glomerular lesionsBillable
- N04.2Nephrotic syndrome with diffuse membranous glomerulonephritis
- N04.20Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecifiedBillable
- N04.21Primary membranous nephropathy with nephrotic syndromeBillable
- N04.22Secondary membranous nephropathy with nephrotic syndromeBillable
- N04.29Other nephrotic syndrome with diffuse membranous glomerulonephritisBillable
- N04.3Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritisBillable
- N04.4Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritisBillable
- N04.5Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritisBillable
- N04.6Nephrotic syndrome with dense deposit diseaseBillable
- N04.7Nephrotic syndrome with diffuse crescentic glomerulonephritisBillable
- N04.8Nephrotic syndrome with other morphologic changesBillable
- N04.9Nephrotic syndrome with unspecified morphologic changesBillable
- N04.ANephrotic syndrome with C3 glomerulonephritisBillable
- N04.BNephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)
Coding notes
- congenital nephrotic syndrome
- lipoid nephrosis
Notes that apply from higher levels
Instructions written at a parent level also apply to N04.
Broader instructions also apply from N00-N08 Glomerular diseases and Chapter 14: Diseases of the genitourinary system.
Codes whose notes reference N04
- Q63Excludes1
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about N04
Is N04 billable?
- No. N04 is a header code. Report one of its more specific subcodes instead.