Q27.0Congenital absence and hypoplasia of umbilical artery

Q27.0 is the ICD-10-CM diagnosis code for congenital absence and hypoplasia of umbilical artery. It belongs to category Q27 (other congenital malformations of peripheral vascular system), block Q20-Q28 (congenital malformations of the circulatory system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q27 (other congenital malformations of peripheral vascular system), Q27.0 is specifically for congenital absence and hypoplasia of umbilical artery. Related codes cover congenital renal artery stenosis (Q27.1), other congenital malformations of renal artery (Q27.2), arteriovenous malformation (peripheral) (Q27.3), congenital phlebectasia (Q27.4), other specified congenital malformations of peripheral vascular system (Q27.8) and congenital malformation of peripheral vascular system, unspecified (Q27.9).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 299 (Peripheral Vascular Disorders with MCC, relative weight 1.5842), DRG 300 (Peripheral Vascular Disorders with CC, relative weight 1.0464) and DRG 301 (Peripheral Vascular Disorders without CC/MCC, relative weight 0.7133), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 747.5 (absence or hypoplasia of umbilical artery).