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ICD-10-CM 2027 diagnosis code

Q87.41Marfan syndrome with cardiovascular manifestations

Not billable — use a more specific code

Q87.41 is a header code, so it can't be reported by itself. Choose one of the 2 more specific codes beneath it.

Code last changed in FY2024 (effective October 1, 2023). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About Q87.41

Q87.41 is the ICD-10-CM diagnosis code for Marfan syndrome with cardiovascular manifestations. It belongs to category Q87 (other specified congenital malformation syndromes affecting multiple systems), block Q80-Q89 (other congenital malformations) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is a header code, so it can't be reported by itself; one of its 2 subcodes must be used instead.

Within Q87.4 (Marfan syndrome), Q87.41 is specifically for Marfan syndrome with cardiovascular manifestations. Related codes cover unspecified (Q87.40), with ocular manifestations (Q87.42) and with skeletal manifestation (Q87.43).

To report this condition, pick the subcode that matches the documentation: Q87.410 (dilation) and Q87.418 (manifestations).

Use an additional code(s) to identify all associated manifestations.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015, and changed in FY2024 (title revised).

Specific codes under Q87.41

Notes that apply from higher levels

Instructions written at a parent level also apply to Q87.41.

› From Q87 Other specified congenital malformation syndromes affecting multiple systems
Use additional code
  • code(s) to identify all associated manifestations

Broader instructions also apply from Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
  • FY2024 (effective 10/1/2023): Title revised — was “Marfan's syndrome with cardiovascular manifestations”

Common questions about Q87.41

Is Q87.41 billable?

No. Q87.41 is a header code. Report one of its more specific subcodes instead.