Q87.40Marfan syndrome, unspecified

Q87.40 is the ICD-10-CM diagnosis code for Marfan syndrome, unspecified. It belongs to category Q87 (other specified congenital malformation syndromes affecting multiple systems), block Q80-Q89 (other congenital malformations) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q87.4, choose Q87.40 (unspecified) only when documentation doesn't support a more specific option: with cardiovascular manifestations (Q87.41), with ocular manifestations (Q87.42) and with skeletal manifestation (Q87.43).

Use an additional code(s) to identify all associated manifestations.

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015, and changed in FY2024 (title revised).

Before ICD-10, this condition was coded in ICD-9-CM as 759.82 (Marfan syndrome).