ICD-10-CM 2027 diagnosis code

Q99.81Usher syndrome

Not billable — use a more specific code

Q99.81 is a header code, so it can't be reported by itself. Choose one of the 5 more specific codes beneath it.

Code last changed in FY2026 (effective October 1, 2025). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About Q99.81

Q99.81 is the ICD-10-CM diagnosis code for Usher syndrome. It belongs to category Q99 (other chromosome abnormalities, not elsewhere classified), block Q90-Q99 (chromosomal abnormalities, not elsewhere classified) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is a header code, so it can't be reported by itself; one of its 5 subcodes must be used instead.

Within Q99.8 (other specified chromosome abnormalities), Q99.81 is specifically for Usher syndrome. Related codes cover other specified chromosome abnormalities (Q99.89).

To report this condition, pick the subcode that matches the documentation: Q99.811 (type 1), Q99.812 (type 2), Q99.813 (type 3), Q99.818 (syndrome) and Q99.819 (unspecified).

Use an additional code to identify any auditory and visual manifestations.

It was added in FY2026, effective October 1, 2025.

Specific codes under Q99.81

Coding notes

Use additional codeAdd a secondary code to fully describe the condition

code to identify any auditory and visual manifestations

Notes that apply from higher levels

Instructions written at a parent level also apply to Q99.81.

Broader instructions also apply from Q90-Q99 Chromosomal abnormalities, not elsewhere classified and Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.

Code history

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2027

FY2026 (effective 10/1/2025): Added
No changes since FY2026.

Common questions about Q99.81

Is Q99.81 billable?: No. Q99.81 is a header code. Report one of its more specific subcodes instead.