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ICD-10-CM 2027 diagnosis code

Q99.811Usher syndrome, type 1

✓ Billable / specificPOA exemptCC — complication/comorbidity

Q99.811 is a valid, billable ICD-10-CM code for usher syndrome, type 1. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.

Code last changed in FY2026 (effective October 1, 2025). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About Q99.811

Q99.811 is the ICD-10-CM diagnosis code for Usher syndrome, type 1. It belongs to category Q99 (other chromosome abnormalities, not elsewhere classified), block Q90-Q99 (chromosomal abnormalities, not elsewhere classified) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q99.81 (Usher syndrome), Q99.811 is specifically for Usher syndrome, type 1. Related codes cover type 2 (Q99.812), type 3 (Q99.813), other Usher syndrome (Q99.818) and unspecified (Q99.819).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC, relative weight 1.4908), DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC, relative weight 0.9783) and DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC, relative weight 0.7378), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It was added in FY2026, effective October 1, 2025.

Notes that apply from higher levels

Instructions written at a parent level also apply to Q99.811.

› From Q99.81 Usher syndrome
Use additional code
  • code to identify any auditory and visual manifestations

Broader instructions also apply from Q90-Q99 Chromosomal abnormalities, not elsewhere classified and Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.

Alphabetic index entries

1 entries

Terms in the official ICD-10-CM index that lead to Q99.811.

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2026 (effective 10/1/2025): Added
  • No changes since FY2026.

Common questions about Q99.811

Is Q99.811 billable?

Yes. Q99.811 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can Q99.811 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict Q99.811 as a principal diagnosis.

Is Q99.811 a CC or MCC?

Q99.811 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.

What DRG does Q99.811 group to?

Q99.811 is used in the MS-DRG v44.0 logic for MS-DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC), MS-DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC) and MS-DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.