ICD-10-CM 2027
ICD-10 code for aciduria
Choose a code from the options below based on the documentation.
From the official ICD-10-CM alphabetic index entry “Aciduria”. Page updated September 29, 2026.
About coding aciduria
The official ICD-10-CM index doesn't give a single default code for aciduria; the code depends on the details below.
More specific aciduria codes (official index)
- 4-hydroxybutyric E72.81 — Disorders of gamma aminobutyric acid metabolism
- argininosuccinic E72.22 — Arginosuccinic aciduria
- gamma-hydroxybutyric E72.81 — Disorders of gamma aminobutyric acid metabolism
- glutaric (type I) E72.3 — Disorders of lysine and hydroxylysine metabolism
- type II E71.313 — Glutaric aciduria type II
- type III E71.5 — Peroxisomal disorders
- orotic (congenital) (hereditary) (pyrimidine deficiency) E79.89 — Other specified disorders of purine and pyrimidine metabolism
- anemia D53.0 — Protein deficiency anemia
Common questions about aciduria ICD-10 codes
What is the ICD-10 code for 4-hydroxybutyric aciduria?
- E72.81 — Disorders of gamma aminobutyric acid metabolism.
What is the ICD-10 code for argininosuccinic aciduria?
- E72.22 — Arginosuccinic aciduria.
What is the ICD-10 code for gamma-hydroxybutyric aciduria?
- E72.81 — Disorders of gamma aminobutyric acid metabolism.
What is the ICD-10 code for glutaric aciduria?
- E72.3 — Disorders of lysine and hydroxylysine metabolism.
What is the ICD-10 code for orotic aciduria?
- E79.89 — Other specified disorders of purine and pyrimidine metabolism.