ICD-10 code for Alymphoplasia

The ICD-10-CM code for Alymphoplasia is D82.1 (Di George's syndrome).

Within D82 (immunodeficiency associated with other major defects), D82.1 is specifically for Di George's syndrome. Related codes cover Wiskott-Aldrich syndrome (D82.0), immunodeficiency with short-limbed stature (D82.2), immunodeficiency following hereditary defective response to Epstein-Barr virus (D82.3), Hyperimmunoglobulin E [IgE] syndrome (D82.4), immunodeficiency associated with other specified major defects (D82.8) and immunodeficiency associated with major defect, unspecified (D82.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 808 (Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCC, relative weight 2.1705), DRG 809 (Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CC, relative weight 1.2262) and DRG 810 (Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCC, relative weight 1.075), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.