ICD-10-CM 2027 diagnosis code
D82.1Di George's syndrome
D82.1 is a valid, billable ICD-10-CM code for di george's syndrome. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.
Looking up by condition? See ICD-10 code for Alymphoplasia, ICD-10 code for DiGeorge's syndrome, ICD-10 code for Di George's syndrome, ICD-10 code for Pharyngeal pouch syndrome.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About D82.1
D82.1 is the ICD-10-CM diagnosis code for Di George's syndrome. It belongs to category D82 (immunodeficiency associated with other major defects), block D80-D89 (certain disorders involving the immune mechanism) and chapter 3 (diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.
Within D82 (immunodeficiency associated with other major defects), D82.1 is specifically for Di George's syndrome. Related codes cover Wiskott-Aldrich syndrome (D82.0), immunodeficiency with short-limbed stature (D82.2), immunodeficiency following hereditary defective response to Epstein-Barr virus (D82.3), Hyperimmunoglobulin E [IgE] syndrome (D82.4), immunodeficiency associated with other specified major defects (D82.8) and immunodeficiency associated with major defect, unspecified (D82.9).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 808 (Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCC, relative weight 2.1705), DRG 809 (Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CC, relative weight 1.2262) and DRG 810 (Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCC, relative weight 1.075), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Before ICD-10, this condition was coded in ICD-9-CM as 279.11 (Digeorge's syndrome).
Coding notes
- Pharyngeal pouch syndrome
- Thymic alymphoplasia
- Thymic aplasia or hypoplasia with immunodeficiency
Notes that apply from higher levels
Instructions written at a parent level also apply to D82.1.
› From D82 Immunodeficiency associated with other major defects
- ataxia telangiectasia [Louis-Bar] (G11.3)
Broader instructions also apply from D80-D89 Certain disorders involving the immune mechanism and Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism.
Alphabetic index entries
12 entriesTerms in the official ICD-10-CM index that lead to D82.1.
- Alymphocytosis › thymic (with immunodeficiency)
- Alymphoplasia, thymic
- Aplasia › parathyroid-thymic
- Aplasia › thymic, with immunodeficiency
- Di George's syndrome
- DiGeorge's syndrome (thymic hypoplasia)
- Dysplasia › thymic, with immunodeficiency
- Hypoplasia, hypoplastic › thymic, with immunodeficiency
- Hypoplasia, hypoplastic › thymus (gland) › with immunodeficiency
- Pharyngeal pouch syndrome
- Syndrome › di George's
- Syndrome › pharyngeal pouch
Codes whose notes reference D82.1
MS-DRG v44.0 grouping
All DRGs →Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.
MDC 16 · Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders
- 808Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCCRW 2.1705
- 809Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CCRW 1.2262
- 810Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCCRW 1.075
ICD-9-CM equivalent
Converter →- 279.11Digeorge's syndromeexact
From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about D82.1
Is D82.1 billable?
- Yes. D82.1 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D82.1 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D82.1 as a principal diagnosis.
Is D82.1 a CC or MCC?
- D82.1 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.
What DRG does D82.1 group to?
- D82.1 is used in the MS-DRG v44.0 logic for MS-DRG 808 (Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCC), MS-DRG 809 (Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CC) and MS-DRG 810 (Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.
What is the ICD-9 code for D82.1?
- The CMS General Equivalence Mappings map D82.1 to ICD-9-CM 279.11.