ICD-10 code for C hemophilia

The ICD-10-CM code for C hemophilia is D68.1 (Hereditary factor XI deficiency).

Within D68 (other coagulation defects), D68.1 is specifically for hereditary factor XI deficiency. Related codes cover von Willebrand disease (D68.0), hereditary deficiency of other clotting factors (D68.2), hemorrhagic disorder due to circulating anticoagulants (D68.3), acquired coagulation factor deficiency (D68.4), primary thrombophilia (D68.5), other thrombophilia (D68.6), other specified coagulation defects (D68.8) and coagulation defect, unspecified (D68.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 813 (Coagulation Disorders, relative weight 1.5257), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.