Skip to content
Dx

ICD-10-CM 2027

ICD-10 code for dystrophy

Choose a code from the options below based on the documentation.

From the official ICD-10-CM alphabetic index entry “Dystrophy, dystrophia”. Page updated September 29, 2026.

About coding dystrophy

The official ICD-10-CM index doesn't give a single default code for dystrophy; the code depends on the details below.

More specific dystrophy codes (official index)

  • adiposogenital E23.6 — Other disorders of pituitary gland
  • autosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker G71.01 — Duchenne or Becker muscular dystrophy
  • Becker's type G71.01 — Duchenne or Becker muscular dystrophy
  • cervical sympathetic G90.2 — Horner's syndrome
  • choroid (hereditary) H31.20 — Hereditary choroidal dystrophy, unspecified
  • central areolar H31.22 — Choroidal dystrophy (central areolar) (generalized) (peripapillary)
  • choroideremia H31.21 — Choroideremia
  • gyrate atrophy H31.23 — Gyrate atrophy, choroid
  • specified type NEC H31.29 — Other hereditary choroidal dystrophy
  • cornea (hereditary) H18.50 — Unspecified hereditary corneal dystrophies
  • endothelial H18.51 — Endothelial corneal dystrophy
  • epithelial H18.52 — Epithelial (juvenile) corneal dystrophy
  • granular H18.53 — Granular corneal dystrophy
  • lattice H18.54 — Lattice corneal dystrophy
  • macular H18.55 — Macular corneal dystrophy
  • specified type NEC H18.59 — Other hereditary corneal dystrophies
  • Duchenne's type G71.01 — Duchenne or Becker muscular dystrophy
  • due to malnutrition E45 — Retarded development following protein-calorie malnutrition
  • Erb's G71.02 — Facioscapulohumeral muscular dystrophy
  • Fuchs' H18.51 — Endothelial corneal dystrophy
  • Gower's muscular G71.01 — Duchenne or Becker muscular dystrophy
  • hair L67.8 — Other hair color and hair shaft abnormalities
  • infantile neuraxonal G31.89 — Other specified degenerative diseases of nervous system
  • Landouzy-Déjérine G71.02 — Facioscapulohumeral muscular dystrophy
  • Leyden-Möbius G71.039 — Limb girdle muscular dystrophy, unspecified
  • meaning Limb girdle muscular dystrophy NOS G71.039 — Limb girdle muscular dystrophy, unspecified
  • meaning Limb girdle muscular dystrophy, other specified type,
  • meaning Limb girdle muscular dystrophy, specified type NEC G71.038 — Other limb girdle muscular dystrophy
  • meaning Limb girdle muscular dystrophy type 2A (autosomal recessive) G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
  • muscular G71.00 — Muscular dystrophy, unspecified
  • autosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker G71.01 — Duchenne or Becker muscular dystrophy
  • benign (Becker type) G71.01 — Duchenne or Becker muscular dystrophy
  • scapuloperoneal with early contractures [Emery-Dreifuss] G71.09 — Other specified muscular dystrophies
  • congenital (hereditary) (progressive) (with specific morphological abnormalities of the muscle fiber) G71.09 — Other specified muscular dystrophies
  • myotonic G71.11 — Myotonic muscular dystrophy
  • distal G71.09 — Other specified muscular dystrophies
  • Duchenne type G71.01 — Duchenne or Becker muscular dystrophy
  • Emery-Dreifuss G71.09 — Other specified muscular dystrophies
  • Erb type G71.02 — Facioscapulohumeral muscular dystrophy
  • facioscapulohumeral G71.02 — Facioscapulohumeral muscular dystrophy
  • Gower's G71.01 — Duchenne or Becker muscular dystrophy
  • hereditary (progressive) G71.09 — Other specified muscular dystrophies
  • Landouzy-Déjérine type G71.02 — Facioscapulohumeral muscular dystrophy
  • limb-girdle G71.039 — Limb girdle muscular dystrophy, unspecified
  • alpha-sarcoglycan-related G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
  • anoctamin-5-related autosomal recessive (R12) G71.035 — Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
  • autosomal recessive NEC G71.038 — Other limb girdle muscular dystrophy
  • beta-sarcoglycan-related G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
  • calpain-3-related G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
  • autosomal dominant G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • autosomal recessive G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
  • collagen VI related
  • autosomal dominant G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • autosomal recessive G71.038 — Other limb girdle muscular dystrophy
  • D1 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • D2 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • D3 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • D4 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • D5 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • delta-sarcoglycan-related G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
  • due to
  • alpha sarcoglycan dysfunction G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
  • anoctamin-5 dysfunction G71.035 — Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
  • beta sarcoglycan dysfunction G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
  • fukutin related protein dysfunction G71.036 — Limb girdle muscular dystrophy due to fukutin related protein dysfunction
  • sarcoglycan dysfunction, specified NEC G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
  • FKRP-related autosomal recessive G71.038 — Other limb girdle muscular dystrophy
  • gamma-sarcoglycan-related G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
  • R1 (autosomal recessive) G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
  • R2 (autosomal recessive) G71.033 — Limb girdle muscular dystrophy due to dysferlin dysfunction
  • R3 (autosomal recessive) G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
  • R4 (autosomal recessive) G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
  • R5 (autosomal recessive) G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
  • R6 (autosomal recessive) G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
  • R7 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R8 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R9 (autosomal recessive) G71.036 — Limb girdle muscular dystrophy due to fukutin related protein dysfunction
  • R10 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R11 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R12 (autosomal recessive) G71.035 — Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
  • R13 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R14 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R15 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R16 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R17 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R18 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R19 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R20 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R21 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R22 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R23 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • R24 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 1 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • type 1A (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • type 1B (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • type 1C (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • type 1E (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • type 1H (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • type 1I (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
  • type 2 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • specified NEC G71.038 — Other limb girdle muscular dystrophy
  • type 2A (autosomal recessive) G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
  • type 2B (autosomal recessive) G71.033 — Limb girdle muscular dystrophy due to dysferlin dysfunction
  • type 2C (autosomal recessive) G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
  • type 2D (autosomal recessive) G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
  • type 2E (autosomal recessive) G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
  • type 2F (autosomal recessive) G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
  • type 2G (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 2H (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 2I (autosomal recessive) G71.036 — Limb girdle muscular dystrophy due to fukutin related protein dysfunction
  • type 2J (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 2K (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 2L (autosomal recessive) G71.035 — Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
  • type 2M (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 2N (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 2O (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 2P (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 2Q (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 2S (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 2T (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • type 2U (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
  • myotonic G71.11 — Myotonic muscular dystrophy
  • progressive (hereditary) G71.09 — Other specified muscular dystrophies
  • Charcot-Marie (-Tooth) type G60.0 — Hereditary motor and sensory neuropathy
  • pseudohypertrophic (infantile) G71.01 — Duchenne or Becker muscular dystrophy
  • scapulohumeral G71.02 — Facioscapulohumeral muscular dystrophy
  • scapuloperoneal G71.09 — Other specified muscular dystrophies
  • severe (Duchenne type) G71.01 — Duchenne or Becker muscular dystrophy
  • specified type NEC G71.09 — Other specified muscular dystrophies
  • myocardium, myocardial
  • myotonic, myotonica G71.11 — Myotonic muscular dystrophy
  • nail L60.3 — Nail dystrophy
  • congenital Q84.6 — Other congenital malformations of nails
  • nutritional E45 — Retarded development following protein-calorie malnutrition
  • ocular G71.09 — Other specified muscular dystrophies
  • oculocerebrorenal E72.03 — Lowe's syndrome
  • oculopharyngeal G71.09 — Other specified muscular dystrophies
  • ovarian N83.8 — Other noninflammatory disorders of ovary, fallopian tube and broad ligament
  • polyglandular E31.8 — Other polyglandular dysfunction
  • reflex (neuromuscular) (sympathetic)
  • retinal (hereditary) H35.50 — Unspecified hereditary retinal dystrophy
  • in
  • lipid storage disorders E75.6 — Lipid storage disorder, unspecified
  • systemic lipidoses E75.6 — Lipid storage disorder, unspecified
  • involving
  • pigment epithelium H35.54 — Dystrophies primarily involving the retinal pigment epithelium
  • sensory area H35.53 — Other dystrophies primarily involving the sensory retina
  • pigmentary H35.52 — Pigmentary retinal dystrophy
  • vitreoretinal H35.51 — Vitreoretinal dystrophy
  • Salzmann's nodular
  • scapuloperoneal G71.09 — Other specified muscular dystrophies
  • skin NEC L98.8 — Other specified disorders of the skin and subcutaneous tissue
  • sympathetic (reflex)
  • cervical G90.2 — Horner's syndrome
  • tapetoretinal H35.54 — Dystrophies primarily involving the retinal pigment epithelium
  • thoracic, asphyxiating Q77.2 — Short rib syndrome
  • unguium L60.3 — Nail dystrophy
  • congenital Q84.6 — Other congenital malformations of nails
  • vitreoretinal H35.51 — Vitreoretinal dystrophy
  • vulva N90.4 — Leukoplakia of vulva
  • yellow (liver)

Common questions about dystrophy ICD-10 codes

What is the ICD-10 code for adiposogenital dystrophy?

E23.6 — Other disorders of pituitary gland.

What is the ICD-10 code for becker's type dystrophy?

G71.01 — Duchenne or Becker muscular dystrophy.

What is the ICD-10 code for cervical sympathetic dystrophy?

G90.2 — Horner's syndrome.

What is the ICD-10 code for choroid dystrophy?

H31.20 — Hereditary choroidal dystrophy, unspecified.

What is the ICD-10 code for cornea dystrophy?

H18.50 — Unspecified hereditary corneal dystrophies (header code; choose a more specific subcode).

What is the ICD-10 code for duchenne's type dystrophy?

G71.01 — Duchenne or Becker muscular dystrophy.

What is the ICD-10 code for erb's dystrophy?

G71.02 — Facioscapulohumeral muscular dystrophy.