ICD-10-CM 2027
ICD-10 code for erythremia
From the official ICD-10-CM alphabetic index entry “Erythremia (acute)”. Page updated September 29, 2026.
About coding erythremia
The ICD-10-CM code for erythremia is C94.0 (Acute erythroid leukemia). The official index lists 2 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on C94.0.
Within C94 (other leukemias of specified cell type), C94.0 is specifically for acute erythroid leukemia. Related codes cover acute megakaryoblastic leukemia (C94.2), mast cell leukemia (C94.3), acute panmyelosis with myelofibrosis (C94.4), myelodysplastic disease, not elsewhere classified (C94.6) and other specified leukemias (C94.8).
To report this condition, pick the subcode that matches the documentation: C94.00 (not having achieved remission), C94.01 (in remission) and C94.02 (in relapse).
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
More specific erythremia codes (official index)
Common questions about erythremia ICD-10 codes
What is the ICD-10 code for erythremia?
- C94.0 — Acute erythroid leukemia (a header code; report a more specific subcode). More specific codes apply when the documentation supports them: D45, D75.1.
What is the ICD-10 code for chronic erythremia?
- D45 — Polycythemia vera.
What is the ICD-10 code for secondary erythremia?
- D75.1 — Secondary polycythemia.
Is C94.0 billable?
- No. C94.0 is a header code. Report one of its more specific subcodes instead.