ICD-10-CM 2027
ICD-10 code for Friedreich's sclerosis
From the official ICD-10-CM alphabetic index entry “Sclerosis, sclerotic › Friedreich's (spinal cord)”. Page updated September 29, 2026.
About coding Friedreich's sclerosis
The ICD-10-CM code for Friedreich's sclerosis is G11.11 (Friedreich ataxia).
Within G11.1 (early-onset cerebellar ataxia), G11.11 is specifically for Friedreich ataxia. Related codes cover unspecified (G11.10) and other early-onset cerebellar ataxia (G11.19).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 058 (Multiple Sclerosis and Cerebellar Ataxia with MCC, relative weight 1.8438), DRG 059 (Multiple Sclerosis and Cerebellar Ataxia with CC, relative weight 1.2002) and DRG 060 (Multiple Sclerosis and Cerebellar Ataxia without CC/MCC, relative weight 0.9247), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Friedreich's sclerosis ICD-10 codes
What is the ICD-10 code for Friedreich's sclerosis?
- G11.11 — Friedreich ataxia.
Is G11.11 billable?
- Yes. G11.11 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G11.11 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G11.11 as a principal diagnosis.
Is G11.11 a CC or MCC?
- G11.11 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.