G11.1Early-onset cerebellar ataxia

G11.1 is the ICD-10-CM diagnosis code for early-onset cerebellar ataxia. It belongs to category G11 (hereditary ataxia), block G10-G14 (systemic atrophies primarily affecting the central nervous system) and chapter 6 (diseases of the nervous system). It is a header code, so it can't be reported by itself; one of its 3 subcodes must be used instead.

Within G11 (hereditary ataxia), G11.1 is specifically for early-onset cerebellar ataxia. Related codes cover congenital nonprogressive ataxia (G11.0), Late-onset cerebellar ataxia (G11.2), cerebellar ataxia with defective DNA repair (G11.3), hereditary spastic paraplegia (G11.4), Hypomyelination - hypogonadotropic hypogonadism - hypodontia (G11.5), leukodystrophy with vanishing white matter disease (G11.6), other hereditary ataxias (G11.8) and unspecified (G11.9).

To report this condition, pick the subcode that matches the documentation: G11.10 (unspecified), G11.11 (ataxia) and G11.19 (ataxia).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015, and changed in FY2021 (expanded into subcodes).

Before ICD-10, this condition was coded in ICD-9-CM as 334.0 (Friedreich's ataxia) and 334.3 (other cerebellar ataxia).