ICD-10-CM 2027
ICD-10 code for Fucosidosis
From the official ICD-10-CM alphabetic index entry “Fucosidosis”. Page updated September 29, 2026.
About coding Fucosidosis
The ICD-10-CM code for Fucosidosis is E77.1 (Defects in glycoprotein degradation).
Within E77 (disorders of glycoprotein metabolism), E77.1 is specifically for defects in glycoprotein degradation. Related codes cover defects in post-translational modification of lysosomal enzymes (E77.0), other disorders of glycoprotein metabolism (E77.8) and disorder of glycoprotein metabolism, unspecified (E77.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Fucosidosis ICD-10 codes
What is the ICD-10 code for Fucosidosis?
- E77.1 — Defects in glycoprotein degradation.
Is E77.1 billable?
- Yes. E77.1 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E77.1 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E77.1 as a principal diagnosis.
Is E77.1 a CC or MCC?
- No. E77.1 is neither a CC nor an MCC under MS-DRG v44.0.