ICD-10-CM 2027
ICD-10 code for great malformation
Choose a code from the options below based on the documentation.
From the official ICD-10-CM alphabetic index entry “Malformation (congenital) › great”. Page updated September 29, 2026.
About coding great malformation
The official ICD-10-CM index doesn't give a single default code for great malformation; the code depends on the details below.
More specific great malformation codes (official index)
- artery Q25.9 — Congenital malformation of great arteries, unspecified
- aorta
- pulmonary artery
- specified type NEC Q25.8 — Other congenital malformations of other great arteries
- vein Q26.9 — Congenital malformation of great vein, unspecified
- anomalous
- portal venous connection Q26.5 — Anomalous portal venous connection
- pulmonary venous connection Q26.4 — Anomalous pulmonary venous connection, unspecified
- partial Q26.3 — Partial anomalous pulmonary venous connection
- total Q26.2 — Total anomalous pulmonary venous connection
- persistent left superior vena cava Q26.1 — Persistent left superior vena cava
- portal vein-hepatic artery fistula Q26.6 — Portal vein-hepatic artery fistula
- specified type NEC Q26.8 — Other congenital malformations of great veins
- vena cava stenosis, congenital Q26.0 — Congenital stenosis of vena cava