Q26.3Partial anomalous pulmonary venous connection

Q26.3 is the ICD-10-CM diagnosis code for partial anomalous pulmonary venous connection. It belongs to category Q26 (congenital malformations of great veins), block Q20-Q28 (congenital malformations of the circulatory system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q26 (congenital malformations of great veins), Q26.3 is specifically for partial anomalous pulmonary venous connection. Related codes cover congenital stenosis of vena cava (Q26.0), persistent left superior vena cava (Q26.1), total anomalous pulmonary venous connection (Q26.2), anomalous pulmonary venous connection, unspecified (Q26.4), anomalous portal venous connection (Q26.5), portal vein-hepatic artery fistula (Q26.6), other congenital malformations of great veins (Q26.8) and congenital malformation of great vein, unspecified (Q26.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 747.42 (partial anomalous pulmonary venous connection).