Q26.5Anomalous portal venous connection

Q26.5 is the ICD-10-CM diagnosis code for anomalous portal venous connection. It belongs to category Q26 (congenital malformations of great veins), block Q20-Q28 (congenital malformations of the circulatory system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q26 (congenital malformations of great veins), Q26.5 is specifically for anomalous portal venous connection. Related codes cover congenital stenosis of vena cava (Q26.0), persistent left superior vena cava (Q26.1), total anomalous pulmonary venous connection (Q26.2), partial anomalous pulmonary venous connection (Q26.3), anomalous pulmonary venous connection, unspecified (Q26.4), portal vein-hepatic artery fistula (Q26.6), other congenital malformations of great veins (Q26.8) and congenital malformation of great vein, unspecified (Q26.9).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 299 (Peripheral Vascular Disorders with MCC, relative weight 1.5842), DRG 300 (Peripheral Vascular Disorders with CC, relative weight 1.0464) and DRG 301 (Peripheral Vascular Disorders without CC/MCC, relative weight 0.7133), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 747.61 (gastrointestinal vessel anomaly).