ICD-10-CM 2027
ICD-10 code for Lafora disease
Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus
From the official ICD-10-CM alphabetic index entry “Lafora disease”. Page updated September 29, 2026.
About coding Lafora disease
The ICD-10-CM code for Lafora disease is G40.C09 (Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus).
Within G40.C0, choose G40.C09 (without status epilepticus) only when documentation doesn't support a more specific option: with status epilepticus (G40.C01).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 023 (Craniotomy with Major Device Implant or Acute Complex CNS Principal Diagnosis with MCC or Antineoplastic Implant or Epilepsy with Neurostimulator, relative weight 5.7444), DRG 100 (Seizures with MCC, relative weight 1.9233) and DRG 101 (Seizures without MCC, relative weight 0.8952), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Lafora disease ICD-10 codes
What is the ICD-10 code for Lafora disease?
- G40.C09 — Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus.
Is G40.C09 billable?
- Yes. G40.C09 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G40.C09 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G40.C09 as a principal diagnosis.
Is G40.C09 a CC or MCC?
- G40.C09 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.