G40.C09Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus

G40.C09 is the ICD-10-CM diagnosis code for Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus. It belongs to category G40 (epilepsy and recurrent seizures), block G40-G47 (episodic and paroxysmal disorders) and chapter 6 (diseases of the nervous system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within G40.C0, choose G40.C09 (without status epilepticus) only when documentation doesn't support a more specific option: with status epilepticus (G40.C01).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 023 (Craniotomy with Major Device Implant or Acute Complex CNS Principal Diagnosis with MCC or Antineoplastic Implant or Epilepsy with Neurostimulator, relative weight 5.7444), DRG 100 (Seizures with MCC, relative weight 1.9233) and DRG 101 (Seizures without MCC, relative weight 0.8952), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It was added in FY2024, effective October 1, 2023.