ICD-10-CM 2027 diagnosis code
G40.C01Lafora progressive myoclonus epilepsy, not intractable, with status epilepticus
G40.C01 is a valid, billable ICD-10-CM code for lafora progressive myoclonus epilepsy, not intractable, with status epilepticus. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.Short description: Lafora progr myoclonus epilepsy, not ntrct, with stat epi
Code last changed in FY2024 (effective October 1, 2023). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About G40.C01
G40.C01 is the ICD-10-CM diagnosis code for Lafora progressive myoclonus epilepsy, not intractable, with status epilepticus. It belongs to category G40 (epilepsy and recurrent seizures), block G40-G47 (episodic and paroxysmal disorders) and chapter 6 (diseases of the nervous system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.
Within G40.C0 (Lafora progressive myoclonus epilepsy, not intractable), G40.C01 is specifically for Lafora progressive myoclonus epilepsy, not intractable, with status epilepticus. Related codes cover without status epilepticus (G40.C09).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 023 (Craniotomy with Major Device Implant or Acute Complex CNS Principal Diagnosis with MCC or Antineoplastic Implant or Epilepsy with Neurostimulator, relative weight 5.7444), DRG 100 (Seizures with MCC, relative weight 1.9233) and DRG 101 (Seizures without MCC, relative weight 0.8952), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
It was added in FY2024, effective October 1, 2023.
Notes that apply from higher levels
Instructions written at a parent level also apply to G40.C01.
› From G40.C Lafora progressive myoclonus epilepsy
- , if applicable, associated conditions such as dementia (F02.8-)
› From G40 Epilepsy and recurrent seizures
- the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled
Broader instructions also apply from Chapter 6: Diseases of the nervous system.
Alphabetic index entries
1 entriesTerms in the official ICD-10-CM index that lead to G40.C01.
MS-DRG v44.0 grouping
All DRGs →Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.
MDC 01 · Diseases and Disorders of the Nervous System
MDC 01 · Diseases and Disorders of the Nervous System
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2024 (effective 10/1/2023): Added
- No changes since FY2024.
Common questions about G40.C01
Is G40.C01 billable?
- Yes. G40.C01 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G40.C01 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G40.C01 as a principal diagnosis.
Is G40.C01 a CC or MCC?
- G40.C01 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.
What DRG does G40.C01 group to?
- G40.C01 is used in the MS-DRG v44.0 logic for MS-DRG 023 (Craniotomy with Major Device Implant or Acute Complex CNS Principal Diagnosis with MCC or Antineoplastic Implant or Epilepsy with Neurostimulator), MS-DRG 100 (Seizures with MCC) and MS-DRG 101 (Seizures without MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.