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ICD-10-CM 2027

ICD-10 code for Mucolipidosis

Choose a code from the options below based on the documentation.

From the official ICD-10-CM alphabetic index entry “Mucolipidosis”. Page updated September 29, 2026.

About coding Mucolipidosis

The official ICD-10-CM index doesn't give a single default code for mucolipidosis; the code depends on the details below.

More specific Mucolipidosis codes (official index)

  • I E77.1 — Defects in glycoprotein degradation
  • II, III E77.0 — Defects in post-translational modification of lysosomal enzymes
  • IV E75.11 — Mucolipidosis IV

Common questions about Mucolipidosis ICD-10 codes

What is the ICD-10 code for i mucolipidosis?

E77.1 — Defects in glycoprotein degradation.

What is the ICD-10 code for iv mucolipidosis?

E75.11 — Mucolipidosis IV.