ICD-10-CM 2027
ICD-10 code for muscular dystrophy
From the official ICD-10-CM alphabetic index entry “Dystrophy, dystrophia › muscular”. Page updated September 29, 2026.
About coding muscular dystrophy
The ICD-10-CM code for muscular dystrophy is G71.00 (Muscular dystrophy, unspecified). The official index lists 97 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on G71.00.
Within G71.0, choose G71.00 (unspecified) only when documentation doesn't support a more specific option: Duchenne or Becker muscular dystrophy (G71.01), Facioscapulohumeral muscular dystrophy (G71.02), limb girdle muscular dystrophies (G71.03) and other specified muscular dystrophies (G71.09).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific muscular dystrophy codes (official index)
- autosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker G71.01 — Duchenne or Becker muscular dystrophy
- benign (Becker type) G71.01 — Duchenne or Becker muscular dystrophy
- scapuloperoneal with early contractures [Emery-Dreifuss] G71.09 — Other specified muscular dystrophies
- congenital (hereditary) (progressive) (with specific morphological abnormalities of the muscle fiber) G71.09 — Other specified muscular dystrophies
- myotonic G71.11 — Myotonic muscular dystrophy
- distal G71.09 — Other specified muscular dystrophies
- Duchenne type G71.01 — Duchenne or Becker muscular dystrophy
- Emery-Dreifuss G71.09 — Other specified muscular dystrophies
- Erb type G71.02 — Facioscapulohumeral muscular dystrophy
- facioscapulohumeral G71.02 — Facioscapulohumeral muscular dystrophy
- Gower's G71.01 — Duchenne or Becker muscular dystrophy
- hereditary (progressive) G71.09 — Other specified muscular dystrophies
- Landouzy-Déjérine type G71.02 — Facioscapulohumeral muscular dystrophy
- limb-girdle G71.039 — Limb girdle muscular dystrophy, unspecified
- alpha-sarcoglycan-related G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
- anoctamin-5-related autosomal recessive (R12) G71.035 — Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
- autosomal recessive NEC G71.038 — Other limb girdle muscular dystrophy
- beta-sarcoglycan-related G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
- calpain-3-related G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
- autosomal dominant G71.031 — Autosomal dominant limb girdle muscular dystrophy
- autosomal recessive G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
- collagen VI related
- autosomal dominant G71.031 — Autosomal dominant limb girdle muscular dystrophy
- autosomal recessive G71.038 — Other limb girdle muscular dystrophy
- D1 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- D2 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- D3 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- D4 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- D5 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- delta-sarcoglycan-related G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
- due to
- alpha sarcoglycan dysfunction G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
- anoctamin-5 dysfunction G71.035 — Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
- beta sarcoglycan dysfunction G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
- fukutin related protein dysfunction G71.036 — Limb girdle muscular dystrophy due to fukutin related protein dysfunction
- sarcoglycan dysfunction, specified NEC G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
- FKRP-related autosomal recessive G71.038 — Other limb girdle muscular dystrophy
- gamma-sarcoglycan-related G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
- R1 (autosomal recessive) G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
- R2 (autosomal recessive) G71.033 — Limb girdle muscular dystrophy due to dysferlin dysfunction
- R3 (autosomal recessive) G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
- R4 (autosomal recessive) G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
- R5 (autosomal recessive) G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
- R6 (autosomal recessive) G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
- R7 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R8 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R9 (autosomal recessive) G71.036 — Limb girdle muscular dystrophy due to fukutin related protein dysfunction
- R10 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R11 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R12 (autosomal recessive) G71.035 — Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
- R13 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R14 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R15 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R16 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R17 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R18 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R19 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R20 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R21 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R22 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R23 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- R24 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 1 (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- type 1A (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- type 1B (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- type 1C (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- type 1E (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- type 1H (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- type 1I (autosomal dominant) G71.031 — Autosomal dominant limb girdle muscular dystrophy
- type 2 (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- specified NEC G71.038 — Other limb girdle muscular dystrophy
- type 2A (autosomal recessive) G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
- type 2B (autosomal recessive) G71.033 — Limb girdle muscular dystrophy due to dysferlin dysfunction
- type 2C (autosomal recessive) G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
- type 2D (autosomal recessive) G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
- type 2E (autosomal recessive) G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
- type 2F (autosomal recessive) G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
- type 2G (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 2H (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 2I (autosomal recessive) G71.036 — Limb girdle muscular dystrophy due to fukutin related protein dysfunction
- type 2J (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 2K (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 2L (autosomal recessive) G71.035 — Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
- type 2M (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 2N (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 2O (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 2P (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 2Q (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 2S (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 2T (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- type 2U (autosomal recessive) G71.038 — Other limb girdle muscular dystrophy
- myotonic G71.11 — Myotonic muscular dystrophy
- progressive (hereditary) G71.09 — Other specified muscular dystrophies
- Charcot-Marie (-Tooth) type G60.0 — Hereditary motor and sensory neuropathy
- pseudohypertrophic (infantile) G71.01 — Duchenne or Becker muscular dystrophy
- scapulohumeral G71.02 — Facioscapulohumeral muscular dystrophy
- scapuloperoneal G71.09 — Other specified muscular dystrophies
- severe (Duchenne type) G71.01 — Duchenne or Becker muscular dystrophy
- specified type NEC G71.09 — Other specified muscular dystrophies
Common questions about muscular dystrophy ICD-10 codes
What is the ICD-10 code for muscular dystrophy?
- G71.00 — Muscular dystrophy, unspecified. More specific codes apply when the documentation supports them: G71.01, G71.01, G71.09, G71.09 and others below.
What is the ICD-10 code for benign muscular dystrophy?
- G71.01 — Duchenne or Becker muscular dystrophy.
What is the ICD-10 code for congenital muscular dystrophy?
- G71.09 — Other specified muscular dystrophies.
What is the ICD-10 code for distal muscular dystrophy?
- G71.09 — Other specified muscular dystrophies.
What is the ICD-10 code for duchenne type muscular dystrophy?
- G71.01 — Duchenne or Becker muscular dystrophy.
What is the ICD-10 code for emery-dreifuss muscular dystrophy?
- G71.09 — Other specified muscular dystrophies.
What is the ICD-10 code for erb type muscular dystrophy?
- G71.02 — Facioscapulohumeral muscular dystrophy.
Is G71.00 billable?
- Yes. G71.00 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G71.00 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G71.00 as a principal diagnosis.
Is G71.00 a CC or MCC?
- No. G71.00 is neither a CC nor an MCC under MS-DRG v44.0.