ICD-10 code for Myofibromatosis

The ICD-10-CM code for Myofibromatosis is D48.19 (Other specified neoplasm of uncertain behavior of connective and other soft tissue). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on D48.19.

Within D48.1, choose D48.19 (Other specified neoplasm of uncertain behavior of connective and other soft tissue) only when documentation doesn't support a more specific option: Desmoid tumor (D48.11).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC, relative weight 1.4908), DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC, relative weight 0.9783) and DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC, relative weight 0.7378), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.