ICD-10-CM 2027
ICD-10 code for pulmonary stenosis
From the official ICD-10-CM alphabetic index entry “Stenosis, stenotic (cicatricial) › pulmonary (artery) (congenital)”. Page updated September 29, 2026.
About coding pulmonary stenosis
The ICD-10-CM code for pulmonary stenosis is Q25.6 (Stenosis of pulmonary artery). The official index lists 13 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q25.6.
Within Q25 (congenital malformations of great arteries), Q25.6 is specifically for stenosis of pulmonary artery. Related codes cover Patent ductus arteriosus (Q25.0), coarctation of aorta (Q25.1), atresia of aorta (Q25.2), Supravalvular aortic stenosis (Q25.3), other congenital malformations of aorta (Q25.4), atresia of pulmonary artery (Q25.5), other congenital malformations of pulmonary artery (Q25.7), other congenital malformations of other great arteries (Q25.8) and 1 more.
As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific pulmonary stenosis codes (official index)
- with ventricular septal defect, transposition of aorta, and hypertrophy of right ventricle Q21.3 — Tetralogy of Fallot
- acquired I28.8 — Other diseases of pulmonary vessels
- in tetralogy of Fallot Q21.3 — Tetralogy of Fallot
- infundibular Q24.3 — Pulmonary infundibular stenosis
- subvalvular Q24.3 — Pulmonary infundibular stenosis
- supravalvular Q25.6 — Stenosis of pulmonary artery
- valve I37.0 — Nonrheumatic pulmonary valve stenosis
- with insufficiency I37.2 — Nonrheumatic pulmonary valve stenosis with insufficiency
- congenital Q22.1 — Congenital pulmonary valve stenosis
- rheumatic I09.89 — Other specified rheumatic heart diseases
- with aortic, mitral or tricuspid (valve) disease I08.8 — Other rheumatic multiple valve diseases
- vein, acquired I28.8 — Other diseases of pulmonary vessels
- vessel NEC I28.8 — Other diseases of pulmonary vessels
Common questions about pulmonary stenosis ICD-10 codes
What is the ICD-10 code for pulmonary stenosis?
- Q25.6 — Stenosis of pulmonary artery. More specific codes apply when the documentation supports them: Q21.3, I28.8, Q21.3, Q24.3 and others below.
What is the ICD-10 code for acquired pulmonary stenosis?
- I28.8 — Other diseases of pulmonary vessels.
What is the ICD-10 code for infundibular pulmonary stenosis?
- Q24.3 — Pulmonary infundibular stenosis.
What is the ICD-10 code for subvalvular pulmonary stenosis?
- Q24.3 — Pulmonary infundibular stenosis.
What is the ICD-10 code for supravalvular pulmonary stenosis?
- Q25.6 — Stenosis of pulmonary artery.
What is the ICD-10 code for valve pulmonary stenosis?
- I37.0 — Nonrheumatic pulmonary valve stenosis.
What is the ICD-10 code for vessel nec pulmonary stenosis?
- I28.8 — Other diseases of pulmonary vessels.
Is Q25.6 billable?
- Yes. Q25.6 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q25.6 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q25.6 as a principal diagnosis.
Is Q25.6 a CC or MCC?
- Q25.6 is an MCC (major complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.