ICD-10-CM 2027
ICD-10 code for Scimitar syndrome
Other congenital malformations of great veins
From the official ICD-10-CM alphabetic index entry “Scimitar syndrome”. Page updated September 29, 2026.
About coding Scimitar syndrome
The ICD-10-CM code for Scimitar syndrome is Q26.8 (Other congenital malformations of great veins).
Within Q26, choose Q26.8 (Other congenital malformations of great veins) only when documentation doesn't support a more specific option: congenital stenosis of vena cava (Q26.0), persistent left superior vena cava (Q26.1), total anomalous pulmonary venous connection (Q26.2), partial anomalous pulmonary venous connection (Q26.3), anomalous pulmonary venous connection, unspecified (Q26.4), anomalous portal venous connection (Q26.5), portal vein-hepatic artery fistula (Q26.6) and congenital malformation of great vein, unspecified (Q26.9).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Scimitar syndrome ICD-10 codes
What is the ICD-10 code for Scimitar syndrome?
- Q26.8 — Other congenital malformations of great veins.
Is Q26.8 billable?
- Yes. Q26.8 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q26.8 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q26.8 as a principal diagnosis.
Is Q26.8 a CC or MCC?
- Q26.8 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.