ICD-10-CM 2027
ICD-10 code for Seitelberger's syndrome
From the official ICD-10-CM alphabetic index entry “Seitelberger's syndrome (infantile neuraxonal dystrophy)”. Page updated September 29, 2026.
About coding Seitelberger's syndrome
The ICD-10-CM code for Seitelberger's syndrome is G31.89 (Other specified degenerative diseases of nervous system).
Within G31.8, choose G31.89 (Other specified degenerative diseases of nervous system) only when documentation doesn't support a more specific option: leukodystrophy, unspecified (G31.80), Alpers disease (G31.81), Leigh's disease (G31.82), neurocognitive disorder with Lewy bodies (G31.83), mild cognitive impairment of uncertain or unknown etiology (G31.84), Corticobasal degeneration (G31.85), Alexander disease (G31.86) and primary progressive apraxia of speech (G31.87).
Use an additional code, if applicable, for codes G31.0-G31.83, G31.85-G31.9, to identify: dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4), dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-), dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3), dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2), dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0) and 1 more.
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
Common questions about Seitelberger's syndrome ICD-10 codes
What is the ICD-10 code for Seitelberger's syndrome?
- G31.89 — Other specified degenerative diseases of nervous system.
Is G31.89 billable?
- Yes. G31.89 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G31.89 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G31.89 as a principal diagnosis.
Is G31.89 a CC or MCC?
- No. G31.89 is neither a CC nor an MCC under MS-DRG v44.0.