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ICD-10-CM 2027

ICD-10 code for telangiectasia

I78.1

Nevus, non-neoplastic

✓ Billable / specific

From the official ICD-10-CM alphabetic index entry “Telangiectasia, telangiectasis (verrucous)”. Page updated September 29, 2026.

About coding telangiectasia

The ICD-10-CM code for telangiectasia is I78.1 (Nevus, non-neoplastic). The official index lists 10 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on I78.1.

Within I78 (diseases of capillaries), I78.1 is specifically for nevus, non-neoplastic. Related codes cover hereditary hemorrhagic telangiectasia (I78.0), other diseases of capillaries (I78.8) and disease of capillaries, unspecified (I78.9).

Don't report I78.1 together with the conditions in its Excludes1 note: nevus NOS (D22.-) and vascular NOS (Q82.5).

The conditions in its Excludes2 note aren't part of I78.1, but may be coded alongside it if the patient has both: blue nevus (D22.-), flammeus nevus (Q82.5), hairy nevus (D22.-), melanocytic nevus (D22.-) and 5 more.

More specific telangiectasia codes (official index)

  • ataxic (cerebellar) (Louis-Bar) G11.3 — Cerebellar ataxia with defective DNA repair
  • familial I78.0 — Hereditary hemorrhagic telangiectasia
  • hemorrhagic, hereditary (congenital) (senile) I78.0 — Hereditary hemorrhagic telangiectasia
  • hereditary, hemorrhagic (congenital) (senile) I78.0 — Hereditary hemorrhagic telangiectasia
  • juxtafoveal H35.07 — Retinal telangiectasis
  • macular H35.07 — Retinal telangiectasis
  • macularis eruptiva perstans D47.01 — Cutaneous mastocytosis
  • parafoveal H35.07 — Retinal telangiectasis
  • retinal (idiopathic) (juxtafoveal) (macular) (parafoveal) H35.07 — Retinal telangiectasis
  • spider I78.1 — Nevus, non-neoplastic

Don't confuse with (Excludes1 for I78.1)

Common questions about telangiectasia ICD-10 codes

What is the ICD-10 code for telangiectasia?

I78.1 — Nevus, non-neoplastic. More specific codes apply when the documentation supports them: G11.3, I78.0, I78.0, I78.0 and others below.

What is the ICD-10 code for ataxic telangiectasia?

G11.3 — Cerebellar ataxia with defective DNA repair.

What is the ICD-10 code for familial telangiectasia?

I78.0 — Hereditary hemorrhagic telangiectasia.

What is the ICD-10 code for juxtafoveal telangiectasia?

H35.07 — Retinal telangiectasis (header code; choose a more specific subcode).

What is the ICD-10 code for macular telangiectasia?

H35.07 — Retinal telangiectasis (header code; choose a more specific subcode).

What is the ICD-10 code for macularis eruptiva perstans telangiectasia?

D47.01 — Cutaneous mastocytosis.

What is the ICD-10 code for parafoveal telangiectasia?

H35.07 — Retinal telangiectasis (header code; choose a more specific subcode).

Is I78.1 billable?

Yes. I78.1 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can I78.1 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict I78.1 as a principal diagnosis.

Is I78.1 a CC or MCC?

No. I78.1 is neither a CC nor an MCC under MS-DRG v44.0.