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ICD-10-CM 2027 diagnosis code

G11.3Cerebellar ataxia with defective DNA repair

✓ Billable / specificCC — complication/comorbidity

G11.3 is a valid, billable ICD-10-CM code for cerebellar ataxia with defective dna repair. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.

Looking up by condition? See ICD-10 code for Louis-Bar syndrome, ICD-10 code for Ataxia-telangiectasia, ICD-10 code for Boder-Sedgwick syndrome.

Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About G11.3

G11.3 is the ICD-10-CM diagnosis code for cerebellar ataxia with defective DNA repair. It belongs to category G11 (hereditary ataxia), block G10-G14 (systemic atrophies primarily affecting the central nervous system) and chapter 6 (diseases of the nervous system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within G11 (hereditary ataxia), G11.3 is specifically for cerebellar ataxia with defective DNA repair. Related codes cover congenital nonprogressive ataxia (G11.0), early-onset cerebellar ataxia (G11.1), Late-onset cerebellar ataxia (G11.2), hereditary spastic paraplegia (G11.4), Hypomyelination - hypogonadotropic hypogonadism - hypodontia (G11.5), leukodystrophy with vanishing white matter disease (G11.6), other hereditary ataxias (G11.8) and unspecified (G11.9).

The conditions in its Excludes2 note aren't part of G11.3, but may be coded alongside it if the patient has both: Cockayne's syndrome (Q87.19), other disorders of purine and pyrimidine metabolism (E79.-) and xeroderma pigmentosum (Q82.1).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 058 (Multiple Sclerosis and Cerebellar Ataxia with MCC, relative weight 1.8438), DRG 059 (Multiple Sclerosis and Cerebellar Ataxia with CC, relative weight 1.2002) and DRG 060 (Multiple Sclerosis and Cerebellar Ataxia without CC/MCC, relative weight 0.9247), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 334.8 (other spinocerebellar diseases).

Coding notes

Applicable toConditions and synonyms classified to this code
  • Ataxia telangiectasia [Louis-Bar]
Excludes2Not included here — may be reported together if both conditions exist
  • Cockayne's syndrome (Q87.19)
  • other disorders of purine and pyrimidine metabolism (E79.-)
  • xeroderma pigmentosum (Q82.1)

Notes that apply from higher levels

Instructions written at a parent level also apply to G11.3.

› From G11 Hereditary ataxia
Excludes2
  • cerebral palsy (G80.-)
  • hereditary and idiopathic neuropathy (G60.-)
  • metabolic disorders (E70-E88)

Broader instructions also apply from Chapter 6: Diseases of the nervous system.

Alphabetic index entries

9 entries

Terms in the official ICD-10-CM index that lead to G11.3.

Codes whose notes reference G11.3

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

ICD-9-CM equivalent

Converter →
  • 334.8Other spinocerebellar diseasesapproximate

From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
  • No changes since FY2016.

Common questions about G11.3

Is G11.3 billable?

Yes. G11.3 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can G11.3 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict G11.3 as a principal diagnosis.

Is G11.3 a CC or MCC?

G11.3 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.

What DRG does G11.3 group to?

G11.3 is used in the MS-DRG v44.0 logic for MS-DRG 058 (Multiple Sclerosis and Cerebellar Ataxia with MCC), MS-DRG 059 (Multiple Sclerosis and Cerebellar Ataxia with CC) and MS-DRG 060 (Multiple Sclerosis and Cerebellar Ataxia without CC/MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.

What is the ICD-9 code for G11.3?

The CMS General Equivalence Mappings map G11.3 to ICD-9-CM 334.8.