ICD-10 code for Usher syndrome

The ICD-10-CM code for Usher syndrome is Q99.819 (Usher syndrome, unspecified). The official index lists 5 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q99.819.

Within Q99.81, choose Q99.819 (unspecified) only when documentation doesn't support a more specific option: type 1 (Q99.811), type 2 (Q99.812), type 3 (Q99.813) and other Usher syndrome (Q99.818).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC, relative weight 1.4908), DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC, relative weight 0.9783) and DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC, relative weight 0.7378), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.