Skip to content
Dx

ICD-10-CM 2027

ICD-10 code for vena cava anomaly

Q26.9

Congenital malformation of great vein, unspecified

✓ Billable / specificCC — complication/comorbidity

From the official ICD-10-CM alphabetic index entry “Anomaly, anomalous (congenital) (unspecified type) › vena cava (inferior) (superior)”. Page updated September 29, 2026.

About coding vena cava anomaly

The ICD-10-CM code for vena cava anomaly is Q26.9 (Congenital malformation of great vein, unspecified).

Within Q26, choose Q26.9 (Congenital malformation of great vein, unspecified) only when documentation doesn't support a more specific option: congenital stenosis of vena cava (Q26.0), persistent left superior vena cava (Q26.1), total anomalous pulmonary venous connection (Q26.2), partial anomalous pulmonary venous connection (Q26.3), anomalous pulmonary venous connection, unspecified (Q26.4), anomalous portal venous connection (Q26.5), portal vein-hepatic artery fistula (Q26.6) and other congenital malformations of great veins (Q26.8).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

Common questions about vena cava anomaly ICD-10 codes

What is the ICD-10 code for vena cava anomaly?

Q26.9 — Congenital malformation of great vein, unspecified.

Is Q26.9 billable?

Yes. Q26.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can Q26.9 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict Q26.9 as a principal diagnosis.

Is Q26.9 a CC or MCC?

Q26.9 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.