E03.1Congenital hypothyroidism without goiter

E03.1 is the ICD-10-CM diagnosis code for congenital hypothyroidism without goiter. It belongs to category E03 (other hypothyroidism), block E00-E07 (disorders of thyroid gland) and chapter 4 (endocrine, nutritional and metabolic diseases). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within E03, choose E03.1 (Congenital hypothyroidism without goiter) only when documentation doesn't support a more specific option: congenital hypothyroidism with diffuse goiter (E03.0), hypothyroidism due to medicaments and other exogenous substances (E03.2), postinfectious hypothyroidism (E03.3), atrophy of thyroid (acquired) (E03.4), myxedema coma (E03.5), other specified hypothyroidism (E03.8) and hypothyroidism, unspecified (E03.9).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 643 (Endocrine Disorders with MCC, relative weight 1.6139), DRG 644 (Endocrine Disorders with CC, relative weight 1.0044) and DRG 645 (Endocrine Disorders without CC/MCC, relative weight 0.7459), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 243 (congenital hypothyroidism).