ICD-10-CM 2027 diagnosis code
G40.CLafora progressive myoclonus epilepsy
G40.C is a header code, so it can't be reported by itself. Choose one of the 2 more specific codes beneath it.
Code last changed in FY2024 (effective October 1, 2023). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About G40.C
G40.C is the ICD-10-CM diagnosis code for Lafora progressive myoclonus epilepsy. It belongs to category G40 (epilepsy and recurrent seizures), block G40-G47 (episodic and paroxysmal disorders) and chapter 6 (diseases of the nervous system). It is a header code, so it can't be reported by itself; one of its 2 subcodes must be used instead.
Within G40 (epilepsy and recurrent seizures), G40.C is specifically for Lafora progressive myoclonus epilepsy. Related codes cover Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset (G40.0), Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures (G40.1), Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures (G40.2), generalized idiopathic epilepsy and epileptic syndromes (G40.3), other generalized epilepsy and epileptic syndromes (G40.4), epileptic seizures related to external causes (G40.5), other epilepsy and recurrent seizures (G40.8), epilepsy, unspecified (G40.9) and 2 more.
To report this condition, pick the subcode that matches the documentation: G40.C0 (not intractable) and G40.C1 (intractable).
It was added in FY2024, effective October 1, 2023.
Specific codes under G40.C
Coding notes
- Lafora body disease
- , if applicable, associated conditions such as dementia (F02.8-)
Notes that apply from higher levels
Instructions written at a parent level also apply to G40.C.
› From G40 Epilepsy and recurrent seizures
- the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled
Broader instructions also apply from Chapter 6: Diseases of the nervous system.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2024 (effective 10/1/2023): Added
- No changes since FY2024.
Common questions about G40.C
Is G40.C billable?
- No. G40.C is a header code. Report one of its more specific subcodes instead.